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Year : 2020  |  Volume : 4  |  Issue : 1  |  Page : 8-12

Cystic fibrosis in asia

1 Department of Pediatrics, Shaheed Suhrawardy Medical College, Dhaka, Bangladesh, India
2 Yee Wui Medical Centre, Macau SAR, China
3 Department of Paediatrics, KK Women's and Children's Hospital, Singapore
4 Department of Paediatrics, University of Medicine, Yangon, Myanmar
5 Department of Pediatrics, Childhood Asthma Atopy Center, Humidifier disinfectant Health Center, Asan Medical Center, University of Ulsan College of Medicine Seoul, Republic of Korea
6 Respirology Division, Child Health Department, Jakarta, Indonesia
7 Department of Pediatrics, Ad-din Women's Medical College, Dhaka, Bangladesh, India
8 Department of Pediatrics, All India Institute of Medical Sciences, New Delhi 110029, India
9 Department of Pediatrics, Ramathibodi Hospital, Mahidol University, Bangkok, Thailand
10 Department of Pediatrics, Pusan National University Yangsan Hospital, Pusan, Republic of Korea
11 Department of Respiratory, Beijing Children's Hospital, Capital Medical University, Beijing, China
12 Department of Pediatric Intensive Care and Respiratory Medicine, Queen Sirikit National Institute of Child Health Bangkok, Thailand
13 Pediatric Interventional Pulmonology Division, Department of Pediatric, Shiraz University of Medical Sciences, Shiraz, Iran
14 Department of Pediatrics, University Malaya, Kuala Lumpur, Malaysia
15 Department of Pediatrics, Hong Kong Sanatorium and Hospital, Hong Kong SAR, China
16 Department of Pediatrics, University of Medicine and Pharmacy at Ho Chi Minh City, Vietnam
17 Kalawati Saran Children Hospital, Lady Hardinge Medical College, New Delhi 110029, India
18 Department of Pediatrics, Nippon Medical School Tama-Nagayama Hospital, Tokyo, Japan
19 Department of Pediatrics, Dr. Sardjito Hospital, Faculty of Medicine, Public Health and Nursing, Universitas Gadjah Mada, Yogyakarta, Indonesia
20 Department of Pediatrics, Kaohsiung Medical University Hospital, Kaohsiung Medical University, Taiwan

Correspondence Address:
S K Kabra
Department of Pediatrics, All India Institute of Medical Sciences, New Delhi - 110 029
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Source of Support: None, Conflict of Interest: None

Read associated Erratum: Erratum: Cystic fibrosis in Asia with this article

DOI: 10.4103/prcm.prcm_5_20

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Background: Cystic fibrosis (CF) is the most common inherited life-limiting illness in the Caucasian population. It is considered to be rare in Asia, but recent reports suggest that CF does occur in Asia. Methods: We carried out a questionnaire-based survey to determine the prevalence of CF across Asian countries and the diagnostic and therapeutic capabilities available in member countries. A questionnaire was sent to member countries of the Asian Pediatric Pulmonology Society. The questionnaire included the total number of children diagnosed with CF seen in the country and the available resources. available resources for diagnosis and management. Results: Fifteen countries responded to the questionnaire. Three countries/regions (Myanmar, Vietnam, and Macau) have not recorded any case of CF. The remaining 12 countries have recorded a variable number of cases which have also been reported in the literature. Sweat chloride testing facilities were available in all the countries except Taiwan that reported cases of CF. Some countries such as India and Bangladesh have developed their own indigenous method for sweat testing. Some countries have facilities for mutation testing. Basic medications such as pancreatic enzyme supplementation and antibiotics were available in all the countries where children with CF have been diagnosed. Inhaled antibiotics and dornase alfa were available only in a few countries. Some other countries reported using the injectable preparation of gentamicin and amikacin for inhalation therapy. Testing for genetic mutation wherever available showed a low frequency of the Delta F 508 mutation which is the most common mutation found in the Caucasian population. Only two countries (India and Japan) have formal CF associations for the affected community. Two countries Japan and China maintain a CF registry, whereas India already started the process of developing it. Conclusion: CF is increasingly being diagnosed over the past two decades in Asian countries. There is a need to create awareness among pediatricians and to develop regional or country-specific protocols and tools for the diagnosis and treatment of children with CF.

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